Pancreatic Cystic Fibroses

《英文msh詞典》Pancreatic Cystic Fibroses
[入口詞] Pancreatic Cystic Fibroses
[主題詞] Cystic Fibrosis
[英文釋義] An inherited disease of exocrine glands,affecting most characteristically the pancreas,respiratory system,and sweat glands,usually beginning in infancy and typified by chronic respiratory infections,pancreatic insufficiency,and susceptibility to heat prostration. Cirrhosis of liver occurring in childhood is common and may produce portal hypertension,splenomegaly,and hypersplenism.